CBS 2019
CBSMD教育中心
中 文

Pulmonary Hypertension

Abstract

Recommended Article

Pulmonary Arterial Hypertension With Abnormal V/Q Single-Photon Emission Computed Tomography Factors associated with pulmonary arterial hypertension (PAH) in systemic sclerosis (SSc) Pulmonary Artery Denervation: An Alternative Therapy for Pulmonary Hypertension Sildenafil added to pirfenidone in patients with advanced idiopathic pulmonary fibrosis and risk of pulmonary hypertension: A Phase IIb, randomised, double-blind, placebo-controlled study - Rationale and study design Exercise unmasks distinct pathophysiologic features in heart failure with preserved ejection fraction and pulmonary vascular disease Left main coronary artery compression in pulmonary hypertension rhACE2 Therapy Modifies Bleomycin-Induced Pulmonary Hypertension via Rescue of Vascular Remodeling Pulmonary Artery Denervation for Patients With Residual Pulmonary Hypertension After Pulmonary Endarterectomy

Clinical Case Study2018 May 23. [Epub ahead of print]

JOURNAL:Int Heart J. Article Link

A Case of Pulmonary Hypertension Associated with Idiopathic Hypereosinophilic Syndrome

Ibe T, Wada H, Sakakura K et al. Keywords: Corticosteroid; Hypereosinophilia; Pulmonary arterial hypertension; Steroid therapy

ABSTRACT

Hypereosinophilic syndrome (HES) is characterized by multi-organ damage that is associated with tissue hypereosinophilia. A persistently elevated eosinophilic count is also required for the diagnosis of HES. Although HES affects various organs, damage to pulmonary artery is rarely reported. We present a case of a 39-year-old man who was diagnosed with pulmonary hypertension (PH) associated with idiopathic HES. Although the pulmonary arterial hypertension specific drugs including intravenous epoprostenol could not control his PH, corticosteroid was effective for both hypereosinophilia and PH. Our case suggests the importance of steroid therapy as well as specific drugs for pulmonary arterial hypertension in the treatment of PH associated with HES.